2-Hydroxyhexanedioic Acid
Accumulation and excretion of 2-Hydroxyhexanedioic Acid (with 2-ketoadipic and 2-aminoadipic) in urine can be caused by 2-ketoadipic acidemia, probably without adverse phenotypic effects , due to deficiency of 2-ketoadipic dehydrogenase.
Supplier | BOC Sciences |
---|---|
Product # | BB014027 |
Pricing | Inquire |
Cas | 18294-85-4 |
Molecular Weight | 162.14 |
Molecular Formula | C6H10O5 |
Canonical SMILES | C(CC(C(=O)O)O)CC(=O)O |