2,5-Dideoxy-2,5-imino-D-mannitol HCl

2,5-Dideoxy-2,5-imino-D-mannitol HCl, a highly efficacious pharmaceutical compound, occupies a prominent position in the biomedical landscape owing to its profound therapeutic value in tackling Fabry disease. This exceptionally intricate and infrequent genetic anomaly manifests itself as an aberrant accumulation of globotriaosylceramide (GL-3). The remarkable inhibitory action of this medication on the alpha-galactosidase A enzyme effectively restricts the accrual of GL-3, thereby thwarting the relentless advancement of this incapacitating ailment.

• Supplier: BOC Sciences
• Product #: 210115-92-7
• Cas: 210115-92-7
• Molecular Weight: 199.63
• Molecular Formula: C6H14ClNO4
• Canonical SMILES: C(C1C(C(C(N1)CO)O)O)O.Cl