Galactosidase Alpha (GLA) Antibody
GLA is a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties.
Supplier | Abbexa Ltd. |
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Product # | abx032961-80UL |
Pricing | 80 µl USD $290.0 |
Clonality | Polyclonal |
Conjugation | Unconjugated |
Host | Rabbit |
Tested Applications | ELISA, WB, IHC, IF/ICC, FCM |
UniProt Primary AC | P06280 |
Dry Ice | No |
Availability | Shipped within 5-10 working days. |
Note | This product is for research use only. |