2-Hydroxy-2-methylbutanoic acid

2-Hydroxy-2-methylbutyric acid is an unusual metabolite found in the urine of patients with 2-hydroxyglutaric aciduria and maple syrup urine disease. 2-Hydroxy-2-methylbutyric acid is also a secondary metabolite found in human urine after exposure to the gasoline additive tert-amyl-Me-ether (TAME).

• Supplier: Selleck Chemicals
• Product #: S6183
• Sku #: S6183-25mg