4,6-Dioxoheptanoic acid-3,4,5,6,7-[13C5]
4,6-Dioxoheptanoic acid-3,4,5,6,7-[13C5] is intended for use as an internal standard for succinylacetone. Succinylacetone is an inhibitor of δ-aminolevulinic acid dehydratase and an abnormal metabolite of tyrosine that accumulates in hereditary tyrosinemia type I, a disorder characterized by a deficiency in fumarylacetoacetate hydrolase (FAH), the final enzyme in tyrosine catabolism.
| Supplier | BOC Sciences |
|---|---|
| Product # | BLP-005740 |
| Pricing | Inquire |
| Molecular Weight | 163.12 |
| Molecular Formula | [13C]5C2H10O4 |
| Canonical SMILES | CC(=O)CC(=O)CCC(=O)O |